Tríada de Carney. Una rara asociación de tumores infrecuentes. Caso clínico

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Miniatura
Fecha
2017-04
Profesor/a Guía
Facultad/escuela
Idioma
es
Título de la revista
ISSN de la revista
Título del volumen
Editor
Sociedad Médica de Santiago
Nombre de Curso
Licencia CC
Licencia CC
Resumen
Carney described a disorder characterized by the presence of several uncommon tumors which were pulmonary chondromas, gastric sarcomas and extra-adrenal paragangliomas. We report a 14 year-old girl in whom multiple gastric tumors were discovered during a study of an iron deficiency anemia and was subjected to a partial gastrectomy. At 25 years of age, she developed several pulmonary chondromas and at 33 years, a mediastinal tumor with features of an extra-adrenal paraganglioma was found. At 35 years of age, a total gastrectomy was performed to remove a gastrointestinal stromal tumor with excision of peritoneal and lymph node metastasis. One year later, the patient died due to liver failure secondary to liver metastases.
Notas
Indexación: Scopus.
Palabras clave
Carney Complex, Chondroma, Leiomyosarcoma, Paraganglioma
Citación
Rev. méd. Chile vol.145 no.4 Santiago Apr. 2017
DOI
Link a Vimeo